Vol. 6, Issue 1, Part A (2024)

Macrodystrophia lipomatosa is localized hypertrophy of a limb or a segment of a limb leading to Gigantism and is a rare cause of congenital macrodactyly, with a disproportionate increase in fibroadipose tissue. It is more common in the foot than in the hand. We present three cases of macrodystrophia lipomatosa (MDL) of the lower limb followed by their surgical management. The first case is a 6 year old female child who presented with bulky pigmented right leg and thigh. We managed this case by growth modulation using a figure of 8 plate. The second case is a 1 year old female child with gigantism of right foot and right leg that was managed by debulking procedure and epiphysiodesis. The third case is of a 9 year old female child with the macrodactyly of the second and third toe on the right side. Epiphysiodesis was done for the second and third toe on the right side.